PDF | Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Undocumented. Very few cases of gigantiform cementoma have been reported, and those associated with a positive family history are especially rare. Confusion exists about the. Familial gigantiform cementoma is a rare benign fibrocemento-osseous lesion of the jaws that can cause severe facial deformity. It has an.
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Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Abstract Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Panoramic radiography showing periapical lesions and missing teeth. Familial gigantiform cementoma with brittle bone disease, pathologic fractures, and osteosarcoma: However, extragnathic presentations of FGC in patients have often been neglected, owing in part to rarity of this disease.
Undocumented radiographic changes and related bone metabolism disorder are herein hypothesized and discussed. References Publications referenced by this paper. Cementoam expansile fibro-osseous lesion in a juvenile.
OMIM Entry – % – GIGANTIFORM CEMENTOMA, FAMILIAL
Fibro-osseous lesions of the face and jaws. NarayanWilfried Wagner Oral surgery, oral medicine, oral pathology and….
We need long-term secure funding to provide you the information that you need at your fingertips. To further identify the specific reasons for multiple fractures alongside these osseous changes previously described, whole-body dual-energy absorptiometry DEA measuring bone mineral density BMD was then offered under permission of the patient and his parents.
Florid osseous dysplasia, which is histologically similar, may be distinct. C Lateral view of FGC. Therefore, we present a case gjgantiform a large FGC family history so as to sketch a more detailed portrait of such ailment.
Gigantiform cementoma – Wikipedia
Gigantiform Cementoma, Familial Search for additional papers on this topic. Fibro-osseous lesions of the head and neck. While the OMIM database is open to the public, users seeking information about a personal medical or genetic condition are urged to consult with a qualified physician for diagnosis and for answers to personal questions. The disorder is usually not expansile, as is familial gigantiform cementoma.
For the latest visit to cementomaa clinic 2 months ago, the outcome in the neomandible region was desirable, and in parallel, the recent DEA test result took a favorable turn as BMD had increased to We might not hastily come to the conclusion that coexistence of FGC and polyostotic pathologic fractures is mere coincidental clinical manifestation.
Articles from Medicine are provided here courtesy of Wolters Kluwer Health. B Preoperative panorex X-ray showed a characteristic radiographic feature of familial gigantiform cementoma FGC with well-circumscribed radiopaque areas involving all quadrants of the jaw, with mandible being more severely damaged. E Postoperative panorex X-ray showed vascularized iliac bone flap for reconstruction. Besides, his pelvis was also gigantifrm to be susceptible to fractures because both cortical and trabecular bones were undergoing a progeric or osteopenic conversion signifying an unexpected calcium loss.
This case report discusses the oral management and faimlial rehabilitation of two patients presenting familial gigantiform cementoma with Ehlers-Danlos Syndrome. F 3-D computed tomography reconstruction of postoperative view. Dentomaxillofac Radiol ; Topics Discussed in This Paper. B Reconstructed computed tomography image of familial gigantiform cementoma appearance.
World Health Organization Classification of Tumours: Citations Giganiform citing this paper.
Incomplete giggantiform or shave-off contouring is not advised because it may cause a possible aggravation or reactivation of rapid FGC growth.
Clinicopathologic presentation of 3 cases. Open in a separate window. Report of a case documented with computed tomography and 3D imaging.
A year-old male patient was referred to our hospital for recurrence of a huge benign tumor in oral cavity. This is an open access article distributed under the Creative Commons Attribution License 4. EllisDerek G. This page was last edited on 11 Octoberat Expert curators review the literature and organize it to facilitate your work.
Familial Gigantiform Cementoma
Clin Radiol ; According to Young et al. Surgical removal of the affected bone is needed, and has to be followed by reconstruction. Unsourced material may be challenged and removed. We are determined to keep this website freely accessible. This article does not cite any sources.
Published online Mar 7. A The adolescent patient’s aunt who had received surgery nonvascularized iliac bone reconstruction 30 years ago now complaint of anterior maxillary mass with chronic infection.